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KMID : 0371619980140020357
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Journal of Wonkwang Medical Science
1998 Volume.14 No. 2 p.357 ~ p.362
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A case of Multiple Malignant Schwannoma associated with Neurofibromatosis
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Park Byoung-Hyun
Ko Hyeck-Jae
Lee Myeung-Su
Kuk Hiang
Koo Ki-Son
Kim Hak-Ryul
Jeong Eun-Taik
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Abstract
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Neurofibromatosis, which was described by von Recklinghausen in 1882, is a hereditary, hamartomatous disorder that primarily involves neuroectoderm and mesoderm. The clinical features are skin manifestations such as cafe-au-lait spots, skeletal manifestations primarily involving vertebrae, central and peripheral nervous manifestations, and other associated abnormalities with increased risk of malignancy. Malignant transformation in neurofibromatosis is estimated at 2-29 %, with malignant schwannoma being the most common malignancy. Malignant schwannoma associated with von Recklinghausen’s disease has been rarely reported in Korea.
We herein report a case of multiple malignant schwannoma associated with neurofibromatosis report this case with a review of literatures.
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KEYWORD
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Neurofibromatosis, Malignant Schwannoma
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